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CCC HD
CCC Hirschsprung Disease
Question | Answer |
---|---|
Hirschsprung Disease (HD) | congenital aganglionic megacolon; mechanical obstruction caused by inadequate motility of part of the intestine |
Incidences of HD | 1/4 cases of neonatal obstruction; occurs in 1 in 5000; four times more common in males than females; may be acute, life-threatening or chronic |
Pathophysiology of HD | absence of ganglion cells, originating from the neural crest in both the anerbac myenteric and Meissner submucosal plexuses of the distal intestine, characterized by fever, abdominal distention, diarrhea, may be severe and lead to dehydration or sepsis |
Diagnosis of HD | diagnosed in the first few months of life, radiographs, full thickness rectal biopsy, and clinical manifestations include: distended abdomen, delay of meconium |
Therapeutic Management of HD | treatment is primarily surgery |
Nursing Care of HD | help parents adjust to congenital defect; foster infant-parent bonding; prepare them for surgical intervention; assist in colostomy care |
Pre-operative care of HD | improve malnourishment; measure abdominal circumference; provide information to parents/family |
Post-operative care of HD | stomal care, andominal post-op care |
Dicharge Care of HD | instruct in colostomy, advocate for family |