click below
click below
Normal Size Small Size show me how
cystic fibrosis
pn 141 test 2 book:burke pg 561
Question | Answer |
---|---|
what is it | an inherited disorder of childhood that causes excess mucous secretions |
what system of the body does it damage most | the lungs |
the genetic defect of CF causes an excess of what | excess mucous production in the lungs |
the mucous plugs what up | small airways |
the plugging of the airways leads to what | atelectasis, infection and bronchiectasis, and ariway dilation |
what happens to the lungs | they become scarred and stiff |
what disorders develop over time | COPD, pulmonary HTN, R sided CHF |
what is pulmonary HTN | increased pressure in the pulmonary vascular system |
what happens with sweat | there is an increased secretion of sodium and chloride in it |
what enzyme are they lacking | a pancreatic enzyme |
s/s of it | dyspnea, chest congestion, chronic cough productive of large amounts of thick sticky sputum, barral chest and clubbing of fingers and toes |
s/s of digestive problems | abd. pain, steatorrhea |
what is steatorrhea | bulky foul smelling stook |
what are treatment goals of CF | preventing and treating respiratory complications and maintaining adequate nutrition |
diagnostic tests: what one Dx it | pilocarpine iontophoresis sweat chloride test |
diagnostic tests: pilocarpine iontophoresis sweat chloride test- what itis | sweat is collected and analyzed for sodium and chloride |
meds: what enzyme is given to improve airway clearence; what does it do | dornase alfa; it liquefies mucus |
meds: why are antibiotics given | prophylactically to prevent recurrent resp. infections |
what transplants help | lung transplants |